A rare disease; Erdheim-Chester disease presenting with spontaneous pneumothorax
TUBERKULOZ VE TORAK-TUBERCULOSIS AND THORAX, cilt.67, sa.3, ss.225-230, 2019 (ESCI, Scopus, TRDizin)
- Yayın Türü: Makale / Tam Makale
- Cilt numarası: 67 Sayı: 3
- Basım Tarihi: 2019
- Doi Numarası: 10.5578/tt.68541
- Dergi Adı: TUBERKULOZ VE TORAK-TUBERCULOSIS AND THORAX
- Derginin Tarandığı İndeksler: Emerging Sources Citation Index (ESCI), Scopus, TR DİZİN (ULAKBİM)
- Sayfa Sayıları: ss.225-230
- Anahtar Kelimeler: Histiocytosis, Erdheim-Chester disease, lung
- Karadeniz Teknik Üniversitesi Adresli: Evet
Özet
Erdheim-Chester disease (ECD) is a rare non-Langerhans histiocytosis of unknown etiology, it is characterized by organ infiltration of foamy histiocytes. Diagnosis of ECD involves the analysis of histiocytes in tissue biopsies: these are typically CD68+ CD1a-. These characteristic histiocytes may be found in almost any tissue in cases of ECD. We present an interesting case of ECD that was presented by spontaneous pneumothorax and neurological involvement.