Outcomes of long term treatments of type I hereditary angioedema in a Turkish family

Akoğlu, GÖKHAN; Kesim, Belgin; Yildiz, Gokhan; Metin, Ahmet

doi:10.1590/abd1806-4841.20175899

Outcomes of long term treatments of type I hereditary angioedema in a Turkish family

Akoğlu G., Kesim B., Yildiz G., Metin A.

ANAIS BRASILEIROS DE DERMATOLOGIA, vol.92, no.5, pp.654-659, 2017 (SCI-Expanded, Scopus)

Publication Type: Article / Article
Volume: 92 Issue: 5
Publication Date: 2017
Doi Number: 10.1590/abd1806-4841.20175899
Journal Name: ANAIS BRASILEIROS DE DERMATOLOGIA
Journal Indexes: Science Citation Index Expanded (SCI-EXPANDED), Scopus
Page Numbers: pp.654-659
Keywords: Complement CI inhibitor protein, Danazol, Hereditary Angioedema Types I and II, C1 INHIBITOR GENE, DANAZOL TREATMENT, ATTENUATED ANDROGENS, THROMBOSIS, MUTATION, ATTACKS, PROPHYLAXIS, CONCENTRATE, DEFICIENCY, EDEMA
Karadeniz Technical University Affiliated: Yes

Abstract

BACKGROUND: Hereditary angioedema is a rare autosomal dominantly inherited immunodeficiency disorder characterized by potentially life-threatening angioedema attacks.