Outcomes of long term treatments of type I hereditary angioedema in a Turkish family
ANAIS BRASILEIROS DE DERMATOLOGIA, cilt.92, sa.5, ss.654-659, 2017 (SCI-Expanded, Scopus)
- Yayın Türü: Makale / Tam Makale
- Cilt numarası: 92 Sayı: 5
- Basım Tarihi: 2017
- Doi Numarası: 10.1590/abd1806-4841.20175899
- Dergi Adı: ANAIS BRASILEIROS DE DERMATOLOGIA
- Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
- Sayfa Sayıları: ss.654-659
- Anahtar Kelimeler: Complement CI inhibitor protein, Danazol, Hereditary Angioedema Types I and II, C1 INHIBITOR GENE, DANAZOL TREATMENT, ATTENUATED ANDROGENS, THROMBOSIS, MUTATION, ATTACKS, PROPHYLAXIS, CONCENTRATE, DEFICIENCY, EDEMA
- Karadeniz Teknik Üniversitesi Adresli: Evet
Özet
BACKGROUND: Hereditary angioedema is a rare autosomal dominantly inherited immunodeficiency disorder characterized by potentially life-threatening angioedema attacks.