Bilateral hip arthroplasty for ochronotic arthropathy


Aynaci O., Onder C. , Turhan A.

CLINICAL RHEUMATOLOGY, vol.19, no.2, pp.150-152, 2000 (Journal Indexed in SCI) identifier identifier identifier

  • Publication Type: Article / Article
  • Volume: 19 Issue: 2
  • Publication Date: 2000
  • Doi Number: 10.1007/s100670050035
  • Title of Journal : CLINICAL RHEUMATOLOGY
  • Page Numbers: pp.150-152

Abstract

Ochronosis is a musculoskeletal manifestation of alkaptonuria, a rare hereditary metabolic disorder characterised by the absence of the enzyme homogentisic acid oxidase and associated with various systemic abnormalities related to the deposition of homogentisic acid pigment (ochronotic pigment). In this report, we describe a 53-year-old, HLA-B27(+) woman with ochronotic arthropathy. In addition to the typical clinical features of the disorder, she had bilateral hip involvement, which was improved by cementless total hip prosthesis.