Thrombotic Thrombocytopenic Purpura in a Patient with Klinefelter Syndrome

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Demircioglu S., Yilmaz S., Bektas Ö., Ceneli O.

ISTANBUL MEDICAL JOURNAL, vol.19, no.2, pp.165-167, 2018 (ESCI) identifier

  • Publication Type: Article / Article
  • Volume: 19 Issue: 2
  • Publication Date: 2018
  • Doi Number: 10.5152/imj.2018.62681
  • Journal Indexes: Emerging Sources Citation Index (ESCI), TR DİZİN (ULAKBİM)
  • Page Numbers: pp.165-167
  • Keywords: Klinefelter syndrome, thrombotic thrombocytopenic purpura, plasma exchange, CANCER
  • Karadeniz Technical University Affiliated: No


Thrombotic thrombocytopenic purpura is a rare disease associated with microangiopathic hemolytic anemia, thrombocytopenia, fever, neurological disorders, and renal insufficiency pentad. It is a fatal hematologic emergency if left untreated. If plasma exchange is feasible, treatment is easy and comfortable. It should be kept in mind that such as in our patient may be acquired at all congenital illnesses.