Malignant melanoma is very rare in the case of oculocutaneous albinism and approximately thirty cases have been reported in the literature. Sixty year old male patient with oculocutaneous albinism was operated four years ago at the right leg due to amelanotic malignant melanoma. The patient taken under follow-up postoperatively, presented with upper gastrointestinal system bleeding. Endoscopic biopsy was reported as malignant melanoma metastasis and than total gastrectomy was performed. There is yet no case with gastric metastasis presenting with oculocutaneous albinism and amelanotic malignant melanoma in the literature. The clinical aspects of this unique case are presented.