Various clinical aspects of DIDMOAD (Wolfram) syndrome


OKTEN A. N., GEDIK Y., DEMIRCI A., MOCAN H., Erduran E., ASLAN Y.

TURKISH JOURNAL OF PEDIATRICS, vol.37, no.3, pp.235-240, 1995 (SCI-Expanded) identifier identifier identifier

  • Publication Type: Article / Article
  • Volume: 37 Issue: 3
  • Publication Date: 1995
  • Journal Name: TURKISH JOURNAL OF PEDIATRICS
  • Journal Indexes: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Page Numbers: pp.235-240
  • Karadeniz Technical University Affiliated: Yes

Abstract

The association of juvenile diabetes mellitus (DM), diabetes insipidus (DI), optic atrophy (OA) and sensorineural deafness (D) is known as DIDMOAD or Wolfram syndrome. Aside from these four cardinal features, a wide variety of abnormalities of the nervous system, urinary tract and endocrine glands have been described in this syndrome.