Pulmonary agenesis associated with dextrocardia, sternal defects, and ectopic kidney


EROGLU A., ALPER F., Turkyilmaz A., KARAOGLANOGLU N., OKUR A.

PEDIATRIC PULMONOLOGY, vol.40, no.6, pp.547-549, 2005 (SCI-Expanded) identifier identifier identifier

  • Publication Type: Article / Article
  • Volume: 40 Issue: 6
  • Publication Date: 2005
  • Doi Number: 10.1002/ppul.20301
  • Journal Name: PEDIATRIC PULMONOLOGY
  • Journal Indexes: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Page Numbers: pp.547-549
  • Keywords: pulmonary agenesis, sternal defect, dextrocardia, ectopic kidney, LUNG
  • Karadeniz Technical University Affiliated: Yes

Abstract

Pulmonary agenesis is a rare embryological defect, usually unilateral, and is associated with skeletal, cardiovascular, and other anomalies. A 22-month-old girl was admitted to our clinic with recurrent pulmonary infections. A chest X-ray and multidetector computed tomography (MDCT) revealed pulmonary agenesis with dextrocardia, sternal defects, and a right pelvic ectopic kidney We report on the first known case of right-sided pulmonary agenesis combined with isolated dextrocardia, sternal defects, and an ectopic kidney The importance of MDCT for the diagnosis of pulmonary agenesis and associated other anomalies is demonstrated.