PEDIATRIC PULMONOLOGY, vol.40, no.6, pp.547-549, 2005 (SCI-Expanded)
Pulmonary agenesis is a rare embryological defect, usually unilateral, and is associated with skeletal, cardiovascular, and other anomalies. A 22-month-old girl was admitted to our clinic with recurrent pulmonary infections. A chest X-ray and multidetector computed tomography (MDCT) revealed pulmonary agenesis with dextrocardia, sternal defects, and a right pelvic ectopic kidney We report on the first known case of right-sided pulmonary agenesis combined with isolated dextrocardia, sternal defects, and an ectopic kidney The importance of MDCT for the diagnosis of pulmonary agenesis and associated other anomalies is demonstrated.