Mutlu M, Dilber E, Asian Y, Okten A, ozturk O. A Turner syndrome case associated with anal atresia, interrupted aortic arch and multicystic dysplastic kidney. Turk J Pediatr 2010; 52: 215-217. Although renal and cardiac malformations are commonly seen in Turner syndrome (TS), anorectal malformations, multicystic dysplastic kidney and interrupted aortic arch are quite rare in TS. A newborn with TS with three quite rare congenital malformations (imperforate anus/anal atresia associated with rectovestibular fistula, interrupted aortic arch, and multicystic dysplastic kidney) is presented.