Cutis laxa-like pseudoxanthoma elasticum with ossification


BAHADIR S. , COBANOGLU U. , SIVILOGLU C., KAPICIOGLU Z., Baykan M.

INTERNATIONAL JOURNAL OF DERMATOLOGY, cilt.43, ss.375-378, 2004 (SCI İndekslerine Giren Dergi) identifier identifier identifier

  • Cilt numarası: 43 Konu: 5
  • Basım Tarihi: 2004
  • Doi Numarası: 10.1111/j.1365-4632.2004.01911.x
  • Dergi Adı: INTERNATIONAL JOURNAL OF DERMATOLOGY
  • Sayfa Sayıları: ss.375-378

Özet

Pseudoxanthoma elasticum (PXE) is a heritable disorder of elastic fibers characterized by yellowish, coalescing papules on the flexural area, which is loose and wrinkled. A 35-year-old woman presented cutis laxa-like marked wrinkling and yellowish papules, and a skin biopsy revealed ossification and fragmentation of elastic fibers in the dermis. Ophthalmologic examination revealed a peau d'orange appearance of the retina. She was also found to have a mitral stenosis and hypertension. This is an unusual case of concurrent ossification and cutis laxa-like PXE.