Rare Factor Deficiencies: A Retrospective, Single-center Cohort Study

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Eroglu N., Erduran E., Bahadır A., Saruhan H.

JOURNAL OF ACADEMIC RESEARCH IN MEDICINE-JAREM, cilt.10, sa.3, ss.232-236, 2020 (ESCI) identifier

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 10 Sayı: 3
  • Basım Tarihi: 2020
  • Doi Numarası: 10.4274/jarem.galenos.2020.3662
  • Dergi Adı: JOURNAL OF ACADEMIC RESEARCH IN MEDICINE-JAREM
  • Derginin Tarandığı İndeksler: Emerging Sources Citation Index (ESCI), TR DİZİN (ULAKBİM)
  • Sayfa Sayıları: ss.232-236
  • Anahtar Kelimeler: Rare factor deficiencies, surgery, factor, BLEEDING DISORDERS
  • Karadeniz Teknik Üniversitesi Adresli: Evet

Özet

Objective: Rare factor deficiencies (RFD) include fibrinogen and factor (F) II, FV, combined FV and FVIII, FVII, FX, FXI, and FXIII deficiencies. Although patients with RFD may present with severe hemorrhage, little is still known about this patient group. Additionally, mortality and morbidity also increase due to the limited available knowledge concerning diagnostic and therapeutic methods and surgical approaches. Herein, we report the demographic features, clinical follow-up, surgical approaches, and treatment of patients with RFD.