Rare Factor Deficiencies: A Retrospective, Single-center Cohort Study

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Eroglu N., Erduran E., Bahadır A., Saruhan H.

JOURNAL OF ACADEMIC RESEARCH IN MEDICINE-JAREM, vol.10, no.3, pp.232-236, 2020 (ESCI) identifier

  • Publication Type: Article / Article
  • Volume: 10 Issue: 3
  • Publication Date: 2020
  • Doi Number: 10.4274/jarem.galenos.2020.3662
  • Journal Name: JOURNAL OF ACADEMIC RESEARCH IN MEDICINE-JAREM
  • Journal Indexes: Emerging Sources Citation Index (ESCI), TR DİZİN (ULAKBİM)
  • Page Numbers: pp.232-236
  • Keywords: Rare factor deficiencies, surgery, factor, BLEEDING DISORDERS
  • Karadeniz Technical University Affiliated: Yes

Abstract

Objective: Rare factor deficiencies (RFD) include fibrinogen and factor (F) II, FV, combined FV and FVIII, FVII, FX, FXI, and FXIII deficiencies. Although patients with RFD may present with severe hemorrhage, little is still known about this patient group. Additionally, mortality and morbidity also increase due to the limited available knowledge concerning diagnostic and therapeutic methods and surgical approaches. Herein, we report the demographic features, clinical follow-up, surgical approaches, and treatment of patients with RFD.