A newly-defined entity: combined pulmonary fibrosis and emphysema syndrome


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Ozcelik N. , Ozsu S.

TUBERKULOZ VE TORAK-TUBERCULOSIS AND THORAX, cilt.63, ss.48-52, 2015 (ESCI İndekslerine Giren Dergi) identifier identifier identifier

  • Cilt numarası: 63 Konu: 1
  • Basım Tarihi: 2015
  • Doi Numarası: 10.5578/tt.7747
  • Dergi Adı: TUBERKULOZ VE TORAK-TUBERCULOSIS AND THORAX
  • Sayfa Sayıları: ss.48-52

Özet

Combined pulmonary fibrosis and emphysema (CPFE) syndrome is a rare disease characterized with shortness of breath, upper lobe emphysema, lower lobe fibrosis and impairment of gas exchange. This syndrome is a disease usually seen in male smokers. Pulmonary hypertension is associated with mortality. Another important feature, spirometric volumes relatively protected and a reduction in carbon monoxide diffusion test. CPFE syndrome in the literature so far have been identified in only 70 patients. In this review CPFE syndrome is presented with literature.