A newly-defined entity: combined pulmonary fibrosis and emphysema syndrome


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Ozcelik N., Ozsu S.

TUBERKULOZ VE TORAK-TUBERCULOSIS AND THORAX, cilt.63, sa.1, ss.48-52, 2015 (ESCI, Scopus, TRDizin) identifier identifier identifier

Özet

Combined pulmonary fibrosis and emphysema (CPFE) syndrome is a rare disease characterized with shortness of breath, upper lobe emphysema, lower lobe fibrosis and impairment of gas exchange. This syndrome is a disease usually seen in male smokers. Pulmonary hypertension is associated with mortality. Another important feature, spirometric volumes relatively protected and a reduction in carbon monoxide diffusion test. CPFE syndrome in the literature so far have been identified in only 70 patients. In this review CPFE syndrome is presented with literature.